Two Cases of Evans Myopathy in a Family.
- Author:
Jung Hee CHO
1
;
Yeon Kyung JUNG
;
Seung Min KIM
;
Il Nam SUNWOO
Author Information
1. Department of Neurology, Yonsei University College of Medicine, Korea. sunwooin@yumc.yonsei.ac.kr
- Publication Type:Case Report
- Keywords:
Evans myopathy;
Malignant hyperthermia
- MeSH:
Fathers;
Humans;
Malignant Hyperthermia;
Muscular Diseases*;
Pathology
- From:Journal of the Korean Neurological Association
2002;20(5):568-570
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Evans myopathy is a type of malignant hyperthermia showing characteristic distribution of myopathic changes. We present two cases of Evans myopathy, father and his son in a family. Five members of this family expired during ane sthesia and surgery and two of these cases were reported as the malignant hyperthermia. The muscle pathology shows moth-eaten appearance with or without unstained cores in NADH-TR stain and its difference between the father and his son is suggestive of rather progressive myopathy than static one. s
