A Case of Lymphangioleiomyomatosis with Pregnancy.
10.4046/trd.1995.42.3.375
- Author:
Seong Ook KIM
1
;
Min Gu KIM
;
Yong Hwan WON
;
Ho Cheol KIM
;
Young Sil HWANG
;
Jong Hwa KIM
Author Information
1. Department of Internal Medicine, College of Medicine, Gyeongsang National University, Chinju, Korea.
- Publication Type:Case Report
- Keywords:
Lymphangioleiomyomatosis;
Pregnancy;
Chylous ascites
- MeSH:
Biopsy;
Chylous Ascites;
Cough;
Dyspnea;
Female;
Follow-Up Studies;
Humans;
Lung;
Lymph Nodes;
Lymphangioleiomyomatosis*;
Medroxyprogesterone;
Myocytes, Smooth Muscle;
Pregnancy*;
Pregnant Women;
Thorax;
Triglycerides
- From:Tuberculosis and Respiratory Diseases
1995;42(3):375-380
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The lymphangioleiomyomatosis(LAM) is a rare disorder, which afflicts mainly young woman of childbearing age, characterized by proliferation of immature smooth muscle cell in the lymphatics. We experienced a case of LAM in 26-years-old pregnant woman, confirmed pathologically by inguinal lymph node biopsy. She has suffered from exertonal dyspnea and dry coughing. The symptoms and chest X-ray were aggravated with pregnancy, but improved after delivery with two times of pregnancy. The chest X-ray showed diffuse reticulonodular infiltration and chest HRCT showed diffuse scattered tiny thin-walled cyst of lung parenchyma. We noted chylous ascites of which triglyceride level is 396 mg/dl. After delivery, the symptoms were getting better. We treated with medroxyprogesterone and planned close observation and follow-up.
