Dentinogenesis imperfecta type II: A case report with 17 years of follow-up.
10.5624/isd.2017.47.2.129
- Author:
Francisco José Reis GAMA
1
;
Isabella Sousa CORRÊA
;
Claudia Scigliano VALERIO
;
Emanuelle de Fátima FERREIRA
;
Flávio Ricardo MANZI
Author Information
1. Department of Oral Health, School of Dentistry, Pontifical Catholic University of Minas Gerais, Belo Horizonte, Brazil.
- Publication Type:Case Report
- Keywords:
Dentinogenesis Imperfecta;
Dental Enamel;
Dentin;
Microscopy, Electron, Scanning
- MeSH:
Amber;
Cell Differentiation;
Crowns;
Dental Enamel;
Dentin;
Dentinogenesis Imperfecta*;
Dentinogenesis*;
Dentists;
Early Diagnosis;
Follow-Up Studies*;
Humans;
Microscopy, Electron, Scanning;
Odontogenesis;
Tooth
- From:Imaging Science in Dentistry
2017;47(2):129-133
- CountryRepublic of Korea
- Language:English
-
Abstract:
Dentinogenesis imperfecta is a dominant autosomal hereditary disorder of dentin formation that affects the deciduous and permanent teeth. Its etiology is characterized by inadequate cell differentiation during odontogenesis. The clinical characteristics of dentinogenesis imperfecta are discolored teeth with a translucency that varies from gray to brown or amber. Radiographically, the teeth exhibit pulp obliteration, thin and short roots, bell-shaped crowns, and periapical bone rarefaction. The aim of this report was to present a case of dentinogenesis imperfecta type II that was followed up over a 17-year period. This report also presents scanning electron microscopy images of the enamel and dentin, showing that both were altered in the affected teeth. The disease characteristics and the treatments that were administered are reported in this study to guide dentists with respect to the need for early diagnosis and adequate follow-up to avoid major sequelae.
