A Case of Uhls Anomaly.
- Author:
Jun Hee SUL
1
;
Ki Chun KIM
;
Ki Sub CHUNG
;
Sung Kyu LEE
;
Chang Jin KIM
;
Jae Yun RHO
Author Information
- Publication Type:Original Article
- MeSH: Autopsy; Ductus Arteriosus, Patent; Heart; Heart Defects, Congenital; Heart Septal Defects, Atrial; Humans; Infant; Korea; Myocardium; Pulmonary Atresia
- From:Journal of the Korean Pediatric Society 1979;22(6):476-480
- CountryRepublic of Korea
- Language:Korean
- Abstract: Congenital hypoplasia of the right ventricular myocardium, also known as parchment heart or Uhl's anomaly, is a rare congenital heart defect. It was first described in Oslers principles and Practice of Medicine in 1905 and reviewed by Segall We found 29 reported cases, but there was no reported case in Korea. Recently, we experienced a case of Uhls anomaly associated with patent ductus arteriosus, atrial septal defect, pulmonary atresia and tricuspid abnormality in a 3 month-old infant, which was confirmed by autopsy. We present a case with a brief review of litteratures.
