A Case of Primary Intestinal Lymphangiectasia.
- Author:
Geun Soo PARK
1
;
Jin Young KWAK
;
Joon Sik KIM
;
Tae Chan KWON
;
Yun Jeong JO
Author Information
1. Department of Pediatrics, Keimyung University, College of Medicine, Taegu, Korea.
- Publication Type:Case Report
- Keywords:
Intestinal lymphangiectasia;
Primary;
Endoscopy
- MeSH:
Agammaglobulinemia;
Biopsy;
Diarrhea;
Diet, Fat-Restricted;
Duodenum;
Edema;
Endoscopy;
Female;
Humans;
Hypoproteinemia;
Infant;
Lymphopenia
- From:Korean Journal of Gastrointestinal Endoscopy
1999;19(4):634-642
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We described a 22-month-old girl, who suffered from a gereralized edema and intermittent diarrhea for 1 month. Intestinal lymphangiectasia was confirmed by endoscopic biopsy. Endoscopic examination revealed showed the characteristic appearance of tiny white flakes scattered in the duodenum, which a histological examination confirmed to be dilated lymph vessels. The other findings from laboratory examinations included lymphopenia, hypoproteinemia, hypogammaglobulinemia and increased fecal a1-antitrypsin clearance. Treatment consisting of a low-fat diet and MCT supplementation was successful. The therapy has resulted in the disappearance of duodenal lesions previously observed endoscopically.
