Anesthetic managements for correction of aortic valve regurgitation in a patient with Loeys-Dietz Syndrome: A case report.
10.4097/kjae.2009.57.3.371
- Author:
Seong Hyop KIM
1
;
Seung Woo BAEK
;
Won Kyoung KWON
;
Duk Kyung KIM
;
Tae Gyoon YOON
;
Jeong Ae LIM
;
Nam Sik WOO
;
Tae Yop KIM
Author Information
1. Department of Anesthesiology and Pain Medicine, Konkuk University School of Medicine, Seoul, Korea. pondkim@unitel.co.kr
- Publication Type:Case Report
- Keywords:
Anesthetic managements;
Aortic valve regurgitation;
Loeys-Dietz Syndrome
- MeSH:
Aneurysm;
Aortic Aneurysm;
Aortic Valve;
Arteries;
Child;
Cleft Palate;
Humans;
Hypertelorism;
Joint Instability;
Loeys-Dietz Syndrome;
Skin Diseases, Genetic;
Uvula;
Vascular Malformations
- From:Korean Journal of Anesthesiology
2009;57(3):371-375
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Loeys-Dietz Syndrome (LDS) is a recently described autosomal dominant aortic aneurysm syndrome with widespread systemic involvement. It is characterized by the triad of 1) arterial tortuosity and aneurysms, 2) hypertelorism, and 3) bifid uvula or cleft palate. A 12-year-old boy with LDS was scheduled to undergo correction of aortic valve regurgitation due to aortic annuloectasia. We report our clinical experiences of a case of LDS patient with brief review of related literatures and relevant anesthetic problems.
