Respiratory failure due to myotonic dystrophy combined with peripartum cardiomyopathy: A case report.
10.4097/kjae.2009.57.3.376
- Author:
Haeng Seon SHIM
1
;
Myoung Keun SHIN
;
Jin Yong CHO
;
In Kyu KIM
;
Seong Ho LEE
Author Information
1. Department of Anesthesiology and Pain Medicine, Masan Samsung Hospital, Sungkyunkwan University School of Medicine, Masan, Korea. smkeun311@yahoo.co.kr
- Publication Type:Case Report
- Keywords:
Myotonic dystrophy;
Peripartum cardiomyopathy;
Respiratory failure
- MeSH:
Cardiomyopathies;
Cataract;
Cesarean Section;
Female;
Heart;
Humans;
Intestines;
Lung;
Muscle Weakness;
Muscles;
Muscular Dystrophies;
Myotonia;
Myotonic Dystrophy;
Peripartum Period;
Pregnancy;
Respiratory Insufficiency
- From:Korean Journal of Anesthesiology
2009;57(3):376-380
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Myotonic dystrophy is an autosomal-dominant inherited neuromuscular disorder that's characterized by slowly progressive muscular dystrophy, muscle weakness and myotonia. The clinical features may vary from just cataracts to involvement of multiple organ systems such as various muscles, the heart, lung and intestine. Its most common complication is postoperative respiratory failure. We encountered a patient who developed sudden unexpected peripartum cardiomyopathy (PPCM) and respiratory failure due to presumed myotonic dystrophy after cesarean section. We report here on our clinical experience with this malady and we include a brief review of the medical literature on myotonic dystrophy.
