Late-onset Segmental Neurofibromatosis on the Face.
- Author:
Joon Won HUH
1
;
Jisook YOO
;
Min Soo KIM
;
Kwang Hyun CHOI
;
Hyang Joon PARK
;
Mihn Sook JUE
Author Information
1. Department of Dermatology, VHS Medical Center, Seoul, Korea. zooooz@hanmail.net
- Publication Type:Case Report
- Keywords:
Face;
Mosaic;
Neurofibromatosis;
Segmental;
Trigeminal nerve
- MeSH:
Neurofibroma;
Neurofibromatoses*;
Neurofibromatosis 1;
Trigeminal Nerve
- From:Korean Journal of Dermatology
2016;54(10):811-813
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Segmental neurofibromatosis is a rare form of neurofibromatosis that is characterized by neurofibromas and/or café au lait macules, limited to one region of the body. The neurofibromas of segmental neurofibromatosis are most commonly occupied by either a cervical or a thoracic dermatome. Segmental neurofibromatosis on the face is extremely rare, and only 10 cases have been described so far. Herein, we report a case of segmental neurofibromatosis on the V1 dermatome for its rarity and unusual location.
