The First Korean Case of Cutaneous Lung Tissue Heterotopia.
10.3346/jkms.2010.25.9.1387
- Author:
Ga Won JEON
1
;
Seong Woo HAN
;
Ji Mi JUNG
;
Mi Seon KANG
;
Jong Beom SIN
Author Information
1. Department of Pediatrics, Inje University College of Medicine, Busan Paik Hospital, Busan, Korea. pedsin@inje.ac.kr
- Publication Type:Case Report
- Keywords:
Choristoma;
Bronchogenic Cyst;
Branchioma;
Skin
- MeSH:
Branchioma/pathology/surgery;
Bronchogenic Cyst/pathology/surgery;
Choristoma/*pathology/surgery;
Humans;
Infant, Newborn;
*Lung;
Magnetic Resonance Imaging;
Male;
Republic of Korea;
Skin Diseases/*pathology/surgery;
Skin Neoplasms/pathology;
Tomography, X-Ray Computed
- From:Journal of Korean Medical Science
2010;25(9):1387-1389
- CountryRepublic of Korea
- Language:English
-
Abstract:
Cutaneous lung tissue heterotopia is a very rare disorder where mature lung tissues develop in the skin. This is only the second known report of cutaneous lung tissue heterotopia, with the first by Singer et al. in 1998. A newborn infant had a hemangioma-like, freely movable mass connected to the anterior aspect of the sternal manubrium. Pathologic findings showed mature lung tissues with bronchi, bronchioles, and alveoli through the dermis and subcutis, and it was diagnosed as cutaneous lung tissue heterotopia. Cutaneous lung tissue heterotopia is hypervascular, so grossly it looks like a hemangioma. It can be differentiated from pulmonary sequestration, teratoma, bronchogenic cyst, and branchial cleft cyst by histology and the location of the mass. We describe the clinical, radiologic, and pathologic findings of a cutaneous lung tissue heterotopia, the first reported in Korea.
