Focal Eosinophilic Myositis Associated with Behçet's Disease.
10.4078/jrd.2017.24.5.303
- Author:
Jung Su EUN
1
;
Jong Wan KANG
;
Jin Young KANG
;
Na Ri KIM
;
Sang Jin LEE
;
Young Mo KANG
;
Man Hoon HAN
;
Eon Jeong NAM
Author Information
1. Division of Rheumatology, Department of Internal Medicine, Kyungpook National University School of Medicine, Daegu, Korea. ejnam@knu.ac.kr
- Publication Type:Case Report
- Keywords:
Behçet's disease;
Idiopathic eosinophilic myopathy;
Focal eosinophilic myositis
- MeSH:
Biopsy;
Diagnosis;
Eosinophilia;
Eosinophils*;
Erythema;
Humans;
Ileum;
Muscle Weakness;
Muscular Diseases;
Myalgia;
Myositis*;
Necrosis;
Regeneration;
Systemic Vasculitis;
Ulcer;
Venous Thrombosis;
Young Adult
- From:Journal of Rheumatic Diseases
2017;24(5):303-308
- CountryRepublic of Korea
- Language:English
-
Abstract:
Behçet's disease (BD) is a systemic vasculitis commonly accompanied by recurrent mucosal ulceration and other systemic manifestations, but rarely by myositis. Focal eosinophilic myositis is the most limited idiopathic eosinophilic myopathy characterized by peripheral blood eosinophilia and/or eosinophilic muscle infiltration. Clinical manifestations include myalgia, muscle weakness, and cutaneous lesions, such as subcutaneous induration and erythema. Given that BD can mimic deep vein thrombosis or pseudotumor, muscle biopsy should be performed to enhance the accuracy of diagnosis. Microscopic examination reveals extensive infiltration of eosinophils and mononuclear cells into muscle, myofiber necrosis, and regeneration. To the best of our knowledge, there have not been any published reports on MEDLINE regarding focal eosinophilic myositis associated with BD. Here, we presented a case of focal eosinophilic myositis associated with intestinal BD in a 23-year-old man who suffered from a large ulcer in the terminal ileum.