A Rare Case of Diffuse Pulmonary Lymphangiomatosis in a Middle-Aged Woman.
10.3348/kjr.2014.15.2.295
- Author:
Hyun Ju LIM
1
;
Joungho HAN
;
Hong Kwan KIM
;
Tae Sung KIM
Author Information
1. Department of Radiology and Center for Imaging, Sungkyunkwan University School of Medicine, Seoul 135-710, Korea.
- Publication Type:Case Reports ; Review
- Keywords:
Lymphangiomatosis;
Interstitial;
Lung;
Computed tomography
- MeSH:
Diagnosis, Differential;
Female;
Humans;
Lung Neoplasms/pathology/*radiography;
Lymphangioma/pathology/*radiography;
Middle Aged;
Rare Diseases/pathology/*radiography;
Tomography, X-Ray Computed
- From:Korean Journal of Radiology
2014;15(2):295-299
- CountryRepublic of Korea
- Language:English
-
Abstract:
Diffuse pulmonary lymphangiomatosis (DPL) is a rare lymphatic disorder characterized by lymphatic channel proliferation. It is mostly reported in children and young adults. Here, we report a case involving a 52-year-old asymptomatic woman who presented with increased interstitial markings, as seen on a chest radiograph. Diffuse interstitial septal thickening was found on a serial follow-up chest computed tomography scan, and lymphangitic metastasis was the primary radiologic differential diagnosis. However, histologic sections of wedge resected lung revealed diffuse pleural and interlobular septal lymphatic proliferation characteristic of DPL.
