Multicentric melanotic neuroectodermal tumor of infancy: a case report.
10.5125/jkaoms.2010.36.5.434
- Author:
Byoung Hwan CHOI
1
;
Su Won PARK
;
Soo Mi JANG
;
Bong Chan PARK
;
Han Na SON
;
Jang Ho SON
;
Iel Yong SUNG
;
Jong Ryoul KIM
;
Yeong Cheol CHO
Author Information
1. Department of Oral and Maxillofacial Surgery, College of Medicine, University of Ulsan, Ulsan, Korea. lovenip@mail.ulsan.ac.kr
- Publication Type:Case Report
- Keywords:
Melanotic neuroectodermal tumor of infancy (MNTI);
Multicentric
- MeSH:
Biopsy;
Brain;
Humans;
Infant;
Infant, Newborn;
Jaw;
Mandible;
Maxilla;
Neuroectodermal Tumor, Melanotic;
Polyenes;
Recurrence
- From:Journal of the Korean Association of Oral and Maxillofacial Surgeons
2010;36(5):434-437
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A melanotic neuroectodermal tumor of infancy (MNTI) is a uncommon osteolytic pigmented neoplasm that primarily affects the jaws of newborn infants. Most patients (> 90%) present with the tumor in the first year of life. Approximately 65% form in the maxilla, 11% in the mandible, 5% in the brain and elsewhere. MNTI is normally benign, but up to 15% may recur and a few have metastasized. Approximately 200 cases of MNTI have been reported but only 2 of them presented as multifocal. A case of MNTI in a 7 month old boy was encountered. The chief complaint was maxillary anterior ridge swelling. The incisional biopsy findings were MNTI. Two months after the first operation, mild swelling of another site was observed. The infant was examined periodically since undergoing two procedures with no recurrence. This case demonstrates the possibility of a multicentric MNTI. We report a multicentric MNTI with a review of the relevant literature.
