A Case of Mesenchymal Hamartoma.
- Author:
Ki Chang LEE
1
;
Chan Jung PARK
;
Woo Ki LEE
;
Kwang Woo KIM
;
Chang Ho CHO
;
Kwang Wha PARK
Author Information
1. Department of Pediatrics, Pohang Sunrin Hospital, Pohang, Korea.
- Publication Type:Case Report
- Keywords:
Mesenchymal hamartoma
- MeSH:
Autopsy;
Bile Ducts;
Connective Tissue;
Cyanosis;
Female;
Hamartoma*;
Humans;
Intestines;
Liver;
Necrosis;
Parturition;
Respiratory Insufficiency;
Ventilators, Mechanical
- From:Journal of the Korean Pediatric Society
1998;41(1):125-128
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
An one-day-old female patient was admitted due to marked abdominal distension, cyanosis, right upper quadrant mass, and respiratory failure since birth. We applied ventilator and supportive care immediatly. However, 4 days later, she was dead due to respiratory failure and hemorragic complication. The radiographic finding showed a huge intra-abdominal mass anterior to the intestine. Autopsy findings showed a huge single cystic tumor in the right lobe of the liver. The cysts were filled with sanguinous fluid. There wasn't any signs of necrosis or calcification. Microscopically, the tumor was well demarcated from the adjacent hepatic parenchyma. It consists of connective tissue with dilated lymphatics, vessels, and bile ducts.