A Case of Tuberous Sclerosis associated with Angiomyolipoma of Kidney and Regional Lymph Nodes.
- Author:
Yeong CHUNG
;
Doo Chan MOON
;
Kyung Sool KWON
;
Tae Ahn CHUNG
- Publication Type:Case Report
- Keywords:
Angiomyolipoma;
Tuberous sclerosis
- MeSH:
Angiomyolipoma*;
Biopsy;
Citrus sinensis;
Female;
Humans;
Kidney*;
Lymph Nodes*;
Lymphatic Diseases;
Skin;
Tomography, X-Ray Computed;
Tuberous Sclerosis*;
Young Adult
- From:Korean Journal of Dermatology
1990;28(3):362-367
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
In tuberous sclerosis angiomyolipomas involving kidney and regional lymph nodes are known to be extremely rare. We report a 21-year-old female, who has had pinhead-sized reddish or brownish papules on the face and skin colored, orange peel like plaques in the lurnbosacral region. She has suffered from tenderness on the left flank since 4 years ago. Abdominal CT scan revealed a large mass in the upper portion of the left kidney and lymphadenopathy of the para-aortic lymph nodes. Biopsy specimens from the mass of the left kidney and regional lymph nodes revealed angiomyolipomas.