A Case of Lymphangioleiomyomatosis with Renal Angiomyolipoma.
10.4046/trd.2001.50.2.245
- Author:
Soon Bock KANG
;
Sung Jin PARK
;
Sang Hoon LEE
;
Do Young JUNG
;
Ji Hoon YOO
;
Jae Yeo KIM
;
In Won PARK
;
Byoung Whui CHOI
;
Dong Sub SON
;
Mee Kyung KIM
- Publication Type:Case Report
- Keywords:
Pulmonary lymphangioleiomyomatosis;
Renal angiomyolipoma;
VATS;
Medroxyprogesterone
- MeSH:
Angiomyolipoma*;
Biopsy;
Diagnosis;
Diagnosis, Oral;
Dyspnea;
Female;
Humans;
Kidney;
Lung;
Lymphangioleiomyomatosis*;
Medroxyprogesterone;
Muscle, Smooth;
Outpatients;
Thoracic Surgery, Video-Assisted;
Thorax;
Tomography, X-Ray Computed
- From:Tuberculosis and Respiratory Diseases
2001;50(2):245-251
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Recently we have experienced one case of pulmonary lymphangioleiomymatosis(LAM). A 49 year-old woman visited the outpatient department complaining of longstanding dyspnea, which was aggravated by exercise. Although the chest PA film showed nothing more than a slight increase in interstitial marking, a lung HRCT revealed multiple cystic lesions of a similar size that were scattered through out the whole field in both lungs. An abdominal CT detected an angiomyolipoma located in the midbody of the left kidney. Video-assisted thoracic surgery(VATS) was performed for the pathologic diagnosis. On gross examination of the biopsy lung, a pulmonary LAM was confirmed by a finding of smooth muscle proliferation in the interstitum of the lung. After the final diagnosis, oral medroxyprogesterone was prescribed and she is presently in a stable condition.
