A Case of VATER Syndrome with Situs Inversus Viscerum Totalis in a Newborn Korean Male Infant.
10.11637/kjpa.1988.1.1.125
- Author:
Chang Sub UHM
;
Young Chul SHIN
- Publication Type:Original Article
- MeSH:
Abdominal Cavity;
Anal Canal;
Aorta, Thoracic;
Appendix;
Cecum;
Ductus Arteriosus, Patent;
Esophageal Atresia;
Heart Septal Defects, Atrial;
Humans;
Infant*;
Infant, Newborn*;
Liver;
Lung;
Male*;
Parturition;
Situs Inversus*;
Spine;
Tracheoesophageal Fistula;
Ureter
- From:Korean Journal of Physical Anthropology
1988;1(1):125-135
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The present report describes a case of VATER syndrome with situs inversus viscerum totalis in a newborn Korean male infant who died immediately after his birth. The disposition of all the organs in thoracic and abdominal cavities formed a complete mirror picture of normal disposition. In addition, the following abnormalities were also present : 1) Unsegmented bar of the 12th thoracic vertebra fused with 11th thoracic vertebra at left side and 1st lumbar vertebra at right side, 2) Imperforated anus (Type 3 of Ladd and Grorss classification), 3) Tracheoesophageal fistula with upper esophageal atresia, 4) Patent ductus arteriosus connected to the descending aorta, 5) Atrial septal defect, septum primum type, 6) Slightly enlarged ureter, 7) Translocation of cecum with appendix beneath the liver, 8) Coiled appendix, 9) Incomplete oblique fissure of the right lung.