A Case of Systemic Lupus Erythematosus with Myelofibrosis.
- Author:
Ju Sang PARK
;
Seong Ho KIM
;
Chan KIM
;
You Sook CHO
;
Bin YOO
;
Hyun Sook CHI
;
Hee Bom MOON
- Publication Type:Case Report
- Keywords:
Myelofibrosis;
Pancytopenia;
Glucocorticoid;
Systemic Lupus Erythematosus
- MeSH:
Adult;
Diagnosis;
Epistaxis;
Humans;
Lupus Erythematosus, Systemic*;
Methylprednisolone;
Pancytopenia;
Prednisolone;
Primary Myelofibrosis*
- From:The Journal of the Korean Rheumatism Association
1998;5(1):108-115
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A 42-year-old man presented with severe pancytopenia and uncontrolled epistaxis. The diagnosis of SLE was made and the pancytopenia was found to be due to myelofibrosis. The pulse therapy with methylprednisolone and maintenance therapy with prednisolone reversed both pancytopenia and myelofibrosis. Although myelofibrosis has been described in SLE, this coexistence must be very rare since there has been only 19 cases showing this combination. We report a case of SLE with myelofibrosis which was reversed by the treatment with glucocorticoid.
