Two Cases of Spontaneous Pneumomediastinum in Dermatomyositis.
- Author:
Jung Sik SONG
;
Yong Beom PARK
;
Jun Gu LEE
;
Ki Hwan KWON
;
Won Ki LEE
;
Chang Hee SUH
;
Chan Hee LEE
;
Chang Ho SONG
;
Ji Soo LEE
;
Soo Kon LEE
- Publication Type:Case Report
- Keywords:
Dermatomyositis;
Pneumomediastinum;
Interstitial lung disease
- MeSH:
Biopsy;
Dermatomyositis*;
Diagnosis;
Exanthema;
Lung Diseases, Interstitial;
Mediastinal Emphysema*;
Muscle, Skeletal;
Muscles;
Myositis;
Neck;
Prognosis;
Recurrence;
Vasculitis
- From:The Journal of the Korean Rheumatism Association
1998;5(1):152-157
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Spontaneous pneumomediastnum has been reported only recently as a rare complication of dermatomyositis. We are reporting two cases of spontaneous pneumomediastinum in dermatomyositis. The diagnosis of dermatomyositis was based on the diagnostic criteria requiring symmetric weakness of limb-girdle muscles and anterior neck flexors, elevation of serum skeletal muscle enzymes, electromyograpic findings of inflammatory myopathy, positive findings on muscle biopsy and dermatologic features including heliotrope rash and Gottron s papule. Vasculitis may be the common denominator leading to the association of dermatomyositis and pneumomediasinum. In reported cases, the prognosis of pneumomediastinum seems unfavorable. Interestingly the 2 cases we are reporting resolved spontaneously without any recurrence.