Inferior Sinus Venosus Type Atrial Septal Defect Initially Presenting Pulmonary Hypertension on Transthoracic Echocardiography.
- Author:
Hyon Joung CHO
1
;
Wook Jin CHUNG
;
Jeong Min BONG
;
Kwen Chul SHIN
;
Mi Seung SHIN
;
Woong Chol KANG
;
Seung Hwan HAN
;
Chan Il MOON
;
Kwang Kon KOH
;
Tae Hoon AHN
;
In Suck CHOI
;
Eak Kyun SHIN
Author Information
- Publication Type:Case Report
- Keywords: Echocardiography; Atrial septal defect; Pulmonary hypertension
- MeSH: Acceleration; Arterial Pressure; Cardiac Catheterization; Cardiac Catheters; Congenital Abnormalities; Dyspnea; Echocardiography; Echocardiography, Transesophageal; Heart Atria; Heart Septal Defects, Atrial; Humans; Hypertension, Pulmonary; Vascular Resistance; Vena Cava, Inferior; Young Adult
- From:Journal of Cardiovascular Ultrasound 2009;17(1):25-27
- CountryRepublic of Korea
- Language:English
- Abstract: Inferior sinus venosus type atrial septal defect (ASD) is a rare congenital cardiac deformity that occurs between the inferior vena cava and right atrium. Inferior sinus venosus defect is difficult to diagnose through transthoracic echocardiography because of its location which is infero-posterior to the fossa ovalis. Increasing pulmonary arterial pressure and pulmonary vascular resistance in patients with sinus venosus defect usually occur earlier than other types of ASD. We report a case of 19-year-old man who presented exertional dyspnea due to inferior sinus venous type ASD with mild pulmonary hypertension. In this case, we found clues from slight diastolic flattening of interventricular septum and shortened acceleration time of right ventricular outflow tract on initial transthoracic echocardiography, leading right heart catheterization and transesophageal echocardiography to reveal this rare type of ASD.
