Modified Starnes Operation for Neonatal Stenotic Ebstein Anomaly.
- Author:
Seung Hyun LEE
1
;
Tae Jin YUN
Author Information
1. Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine. tjyun@amc.seoul.kr
- Publication Type:Case Report
- Keywords:
Congenital heart disease;
Ebstein's anomaly;
Surgery method
- MeSH:
Anoxia;
Brachiocephalic Trunk;
Ebstein Anomaly*;
Emergencies;
Heart Atria;
Heart Bypass, Right;
Heart Defects, Congenital;
Heart Failure;
Heart Ventricles;
Humans;
Polytetrafluoroethylene;
Pulmonary Artery;
Sutures;
Transplants;
Tricuspid Valve
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2005;38(9):633-636
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Sixteen-day-old baby with severe Ebstein anomaly underwent emergency operation to relieve progressive hypoxia and congestive heart failure. Operative findings showed huge right atrium and atrialized right ventricle (aRV) with very small functional RV by distal displacement of tricuspid valve mechanism. We elected to perform modified Starnes operation because biventricular repair was deemed unattainable. After pulmonary and tricuspid valves were primarily closed, aRV was obliterated with multiple sutures from RV apex to the base. Then a PTFE (Gore-Tex, USA) vascular graft was interposed between innominate artery and main pulmonary artery for systemic to pulmonary shunt. The patient was discharged uneventfully, and received bi-directional cavopulmonary shunt 6 months later.
