Supravalvular Aortic Stenosis with Aortic Regurgitation.
- Author:
Jung Tae KIM
1
;
Cheol Joo LEE
;
Dong Moon SOH
;
Jung Sun HAN
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Ajou University School of Medicine.
- Publication Type:Original Article
- Keywords:
Aortic stenosis, supravalvular;
Aortic valve, insuficiency;
Aortic valve, replacement
- MeSH:
Aorta;
Aortic Stenosis, Supravalvular*;
Aortic Valve;
Aortic Valve Insufficiency*;
Coronary Sinus;
Coronary Vessels;
Female;
Humans
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
1999;32(6):591-594
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Supravalvular aortic stenosis is an uncommon, congenital narrowing of the ascending aorta which originates just distal to the level of the ostium of the coronary artery. We conducted a successful surgical treatment in a 39 year- old female patient with a congenital supravalvular aortic stenosis and aortic regurgitation who did not show signs of William's syndrome. After we performed an inverted Y-shaped aortotomy toward the noncoronary sinus and right coronary sinus, pantaloon shaped prosthetic patch(Vascutek, Ino, USA) was used to repair the narrowing sinotubular junction. The aortic valve was replaced concommittently using Sorin Bicarbon 19mm. Her postoperative course was uneventful. The patient discharged at 9th postoperative day in good health.
