Groenblad-Strandberg's Syndrome.
- Author:
Gee Yong CHOE
1
;
Woo Jin CHOE
;
Jae Choon JO
Author Information
1. Department of Ophthalmology, School of Medicine, Pusan National University, Pusan, Korea.
- Publication Type:Case Report
- MeSH:
Alkaline Phosphatase;
Calcium;
Cardiovascular System;
Exudates and Transudates;
Hemorrhage;
Heredity;
Macular Degeneration;
Pelvic Bones;
Phosphorus;
Pseudoxanthoma Elasticum;
Retina;
Retinaldehyde;
Skull
- From:Journal of the Korean Ophthalmological Society
1969;10(1):43-48
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Authors presented two cases of typical Groenblad-Strandberg's syndrome and reviewed concerning pathogenesis, histology, heredity and its related conditions. Followings are to be considered in these cases. 1. Pseudoxanthoma elasticum, generally considered; mainly appears from 25 to 50 years of life, but we met in case 2 that he was eleven years old. 2. In ocular complications Case 1 showed disciform macular degeneration of the left eye and macular hemorrhages in superficial layers of retina of the right eye. The other case was several retinal exudates of the left eye without any amcular complications. 3. Case 2 had suggestive signs of Paget's disease in radiograms of the skull and pelvic bone. Routine laboratery studies including serum calcium, phosphorus and alkaline phosphatase were normal. 4. Suspicious heroditary occurrence was noted in case 2. 5. There were no significant abnormalities in blood and cardiovascular system.
