Proximal Interruption of Right Pulmonary Artery with a Remnant of Patent Ductus Arteriosus.
- Author:
Jung Hyun LEE
1
;
June HUH
;
I Seok KANG
;
Heung Jae LEE
Author Information
1. Department of Pediatrics, Sungkyunkwan University School of Medicine, Seoul, Korea. herzhuh@smc.samsung.co.kr
- Publication Type:Case Report
- Keywords:
Pulmonary artery;
Interruption;
Remnant;
Patent ductus arteriosus
- MeSH:
Bronchiectasis;
Ductus Arteriosus, Patent*;
Hemoptysis;
Humans;
Hypertension, Pulmonary;
Lung;
Pneumonia;
Pulmonary Artery*;
Pulmonary Circulation
- From:Journal of the Korean Pediatric Cardiology Society
2006;10(2):211-215
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Proximal interruption of unilateral pulmonary artery is an uncommon developmental anomaly. Patients without associated cardiac defects may remain asymptomatic but many develop recurrent pulmonary infections, hemoptysis, pneumonitis, bronchiectasis or pulmonary hypertension. We herein reported two cases of interruption of right pulmonary artery which were diagnosed beyond infancy. A remnant of patent ductus arteriosus was revealed on an angiogram in both cases. Surgical intervention could not be considered due to severe hypoplastic right pulmonary artery. Early surgical intervention should be considered to rescue a pulmonary circulation and prevent secondary lung hypoplasia.
