A Case of Pleomorphic Liposarcoma Originating from Mesentery.
10.4166/kjg.2015.65.3.182
- Author:
Jin Young CHOI
1
;
Ji Eun KIM
;
Seung Min LEE
;
Ho Jun KANG
;
Ji Hee SUNG
;
Byung Sung KOH
;
Ju Sang PARK
;
Il Dong KIM
;
So Ya BAIK
Author Information
1. Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea. parkjs@dmc.or.kr
- Publication Type:Case Reports
- Keywords:
Liposarcoma, pleomorphic;
Mesentery
- MeSH:
Aged;
Humans;
Liposarcoma/*diagnosis/pathology/surgery;
Male;
Mesentery/*pathology;
Peritoneal Neoplasms/*diagnosis/pathology/surgery;
Tomography, X-Ray Computed
- From:The Korean Journal of Gastroenterology
2015;65(3):182-185
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Liposarcoma is one of the most common soft tissue sarcomas that occurs in adults and is currently divided into five main subgroups: well-differentiated, myxoid, round cell, pleomorphic, and dedifferentiated. Primary mesenteric liposarcoma is extremely rare, and the treatment strategy is surgical resection with a wide free margin, often followed by radiation and adjuvant chemotherapy if distant metastasis is not detected. A 73-year-old male patient presented with lower abdominal distension. Abdominal CT scan revealed a large homogeneously enhancing mass lesion abutting the sigmoid colon and urinary bladder. At laparotomy, the solid mass measured 28x26x12 cm in size, was well-demarcated, and originated from the mesentery of the middle ileum. It was removed along with some small intestine (ileocecal valve upper 50-150 cm) and ileal mesentery because of adhesion. Histologically, the tumor proved to be pleomorphic liposarcoma. The patient did not undergo any adjuvant treatment following surgery, but he remains disease free until 33 months after surgery. Herein, we report a case of pleomorphic liposarcoma arising from small bowel mesentery.