A Case of Overlap Syndrome with Auoimmune Hepatitis and Cholangiopathy in a Child.
- Author:
Ji A JUNG
1
;
In Keun KWAK
;
Hae Ran LEE
;
Soo Hee JANG
;
Kyung Mo KIM
;
Eun Sil YOO
Author Information
1. Department of Pediatrics, Hallym University College of Medicine, Korea. asonsum@hallym.or.kr
- Publication Type:Case Report
- Keywords:
Autoimmune overlap syndrome;
Autoimmune hepatitis;
Autoimmune cholangiopathy;
Children
- MeSH:
Child*;
Cholangitis, Sclerosing;
Diagnosis;
Hepatitis*;
Hepatitis, Autoimmune;
Humans;
Liver Cirrhosis, Biliary;
Liver Diseases;
Male
- From:Korean Journal of Pediatric Gastroenterology and Nutrition
2006;9(2):269-275
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Although autoimmune liver diseases are common in Western countries, only sporadic cases have been reported in Korean children. Autoimmune hepatitis, primary biliary cirrhosis, autoimmune cholangiopathy and primary sclerosing cholangitis are major classes of liver diseases currently considered autoimmune. The overlap syndrome has features associated with both autoimmune hepatitis and other liver diseases. We treated a case of the overlap syndrome that included auoimmune hepatitis and cholangiopathy in a 12 year-old boy. Considering that these entities, autoimmune liver diseases or overlap syndromes, are potentially treatable diseases in children, a high index of suspicion is needed for the appropriate diagnosis.
