Multiple Plexiform Schwannomas Associated with Neurofibromatosis Type 2: A case report.
- Author:
Ho Sung PARK
;
Myoung Ja CHUNG
;
Myoung Jae KANG
;
Dong Geun LEE
;
Byung Cook AHN
- Publication Type:Case Report
- Keywords:
Plexiform schwannoma;
Neurofibromatosis type 2
- MeSH:
Meningioma;
Neurilemmoma*;
Neurofibroma, Plexiform;
Neurofibromatoses*;
Neurofibromatosis 1;
Neurofibromatosis 2*;
Neuroma, Acoustic;
Peripheral Nerves
- From:Korean Journal of Pathology
2000;34(5):389-392
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Plexiform schwannoma is a rare benign tumor arising from the peripheral nerve sheath and characterized by a multinodular and plexiform growth pattern. This tumor usually arises sporadically. In rare cases, plexiform schwannomas have been associated with neurofibromatosis type 2. Plexiform schwannoma should be differentiated from plexiform neurofibroma, because the latter is pathognomonic tumor of neurofibromatosis type 1 and has a potential of malignant transformation. We report a case of multiple plexiform schwannomas associated with bilateral acoustic neuromas and meningioma.
