A Case of angioimmunoblastic Lymphadenopathy with Dysproteinemia.
- Author:
Hong Jig KIM
;
Young Keun KIM
;
Hyung Chan PYO
- Publication Type:Case Report
- Keywords:
Angioimmunoblastic lymphadenopathy;
Dysproteinemia
- MeSH:
Anemia;
Biopsy;
Bone Marrow;
Drug Therapy;
Eosinophils;
Fever;
Hepatomegaly;
Humans;
Immunoblastic Lymphadenopathy*;
Lymph Nodes;
Lymphatic Diseases;
Male;
Middle Aged;
Skin;
Thrombocytopenia;
Vasculitis
- From:Korean Journal of Dermatology
1987;25(4):546-552
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We present a case of angioimmunoblastic lymphadenopathy with dysproteinemia (AILD) in a 57-year-old male who had suffered from fever and general weakness of one month's duration. He showed generalized lymphadenopathy, hepatomegaly and purpuric maculopapules on the whole body surface. Lahoratory findings show anemia, polyclonal gammaglobulinemia and thrombocytopenia. The lymph node biopsy specimens show morphologic triad of AILD except lack of interstitial deposits of eosinophilic materials and the skin biopsy specimen shows lymphohistiocytic vasculitis. Bone marrow biopsy specimen shows similar findings in lymph node, suggesting bone marrow involvement. He have been treated with COPP chemotherapy.