Pulmonary Arteriovenous Fistula: Clinical and Histologic Spectrum of Four Cases.
- Author:
Soomin AHN
1
;
Joungho HAN
;
Hong Kwan KIM
;
Tae Sung KIM
Author Information
- Publication Type:Case Report
- Keywords: Lung; Arteriovenous fistula; Arteriovenous malformations
- MeSH: Aneurysm; Arteriovenous Fistula*; Arteriovenous Malformations; Cystic Adenomatoid Malformation of Lung, Congenital; Diagnosis; Fistula; Hand; Hemodynamics; Lung; Pulmonary Artery; Pulmonary Veins
- From:Journal of Pathology and Translational Medicine 2016;50(5):390-393
- CountryRepublic of Korea
- Language:English
- Abstract: Pulmonary arteriovenous fistula (PAVF) is abnormally dilated vessels that provide a right-to-left shunt between pulmonary artery and pulmonary vein and is clinically divided into simple and complex type. Here, we report four cases of surgically resected sporadic PAVFs presenting various clinical and histologic spectrums. Cases 1 (a 57-old-female) and 2 (a 54-old-female) presented as incidentally identified single aneurysmal fistulas and the lesions were surgically removed without complication. On the other hand, case 3 (an 11-old-male) showed diffuse dilated vascular sacs involving both lungs and caused severe hemodynamic and pulmonary dysfunction. Embolization and surgical resection of the main lesion failed to relieve the symptoms. Case 4 (a 36-old-male) had a localized multiloculated cyst clinically mimicking congenital cystic adenomatoid malformation. Microscopically, the lesion consisted of dilated thick vessels, consistent with the diagnosis of fistulous arteriovenous malformation/hemangioma.
