Localized Fibrosing Mediastinitis with Superior Vena Caval(SVC) Syndrome.
10.4046/trd.2007.63.4.387
- Author:
Sang Yun SHIN
1
;
Beom Kyung KIM
;
Byung Hoon PARK
;
Seon Cheol PARK
;
Jun Chul PARK
;
Myoung Kyun SOON
;
Seung Yul LEE
;
Eui IM
;
Han Ho JEON
;
Kyung Soo JUNG
;
Jae Heon JEONG
;
Yu Ri CHOI
;
Kyoung Hoon KANG
;
Yoon Jung CHOI
;
Yong Kook HONG
;
Chong Ju KIM
Author Information
1. Department of Internal Medicine, National Health Insurance Corporation Ilsan Hospital, Koyang, Korea. kom2d@netsgo.com
- Publication Type:Case Report
- Keywords:
Fibrosing mediastinitis;
Superior vena caval syndrome
- MeSH:
Autoimmune Diseases;
Biopsy;
Histoplasmosis;
Mediastinitis*;
Mediastinum;
Rare Diseases;
Transplants;
Tuberculosis
- From:Tuberculosis and Respiratory Diseases
2007;63(4):387-391
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Fibrosing mediastinitis is a rare disease that is characterized by the proliferation of dense fibrous tissue of the mediastinum. The pathogenesis of fibrosing mediastinitis is unknown in most cases. However, histoplasmosis, tuberculosis, autoimmune disease, radiation therapy, and other idiopathic fibroinflammatory diseases have been implicated in some cases. Most clinical features are related to an obstruction or compression of the mediastinal structure. Fibrosing mediastinitis is often progressive and occurs diffusely throughout the mediastinum. We encountered a case of fibrosing mediastinitis of a very focal lesion without evidence of mediastinal involvement. The condition was confirmed by biopsy and graft bypass surgery was performed because of SVC syndrome.
