Pulmonary Artery Intimal Sarcoma with Lung Metastasis.
- Author:
In Sub KIM
1
;
Sung Chol JUNG
;
Woo Shik KIM
;
Yun Suk BAE
;
Young Chul SHIN
;
Shng Hyuk CHUNG
;
Hwan Kook YOO
;
Jung Ho LEE
;
Byung Yul KIM
Author Information
1. Department of Thoracic & Cardiovascular Surgery, National Medical Center, Korea. alien772@freechal.com
- Publication Type:Case Report
- Keywords:
Hemangiosarcoma;
Pulmonary arteries
- MeSH:
Autopsy;
Cardiopulmonary Bypass;
Diagnosis;
Drug Therapy;
Hemangiosarcoma;
Humans;
Lung*;
Middle Aged;
Neoplasm Metastasis*;
Pericardium;
Polytetrafluoroethylene;
Pulmonary Artery*;
Pulmonary Embolism;
Rare Diseases;
Sarcoma*;
Thrombosis;
Transplants
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2003;36(12):979-984
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Primary pulmonary artery sarcoma is very rare disease. The diagnosis of pulmonary artery sarcoma is frequently confused with pulmonary embolism because its clinical symptom and radiologic findings are similar with pulmonary embolism. It was often diagnosed at autopsy as it progresses rapidly. So Pulmonary artery sarcoma must be suspected if the origin of thrombus is not known and anticoagulation therapy is not effective. In this case, a 57 years old man who has been diagnosed pulmonary embolism was transferred to our department because of ineffective anticoagulant therapy and its worsening lesion despite of 5 month-therapy. In operative findings, it was pulmonary artery sarcoma that invaded to pericardium. There was angiosarcoma in right pulmonary artery, which metastasized to lung parenchyme. Under cardiopulmonary bypass, we resected main pulmonary artery and right lung. The Gore-tex graft was interposed between main pulmonary artery and left pulmonary artery. He was discharged after chemotherapy.
