A Case of Malignant Extrarenal Rhabdoid Tumor of the Retroperitoneum.
- Author:
Seong A KIM
1
;
Ja Hyun HONG
;
Chuhl Joo LYU
;
Chang Hyun YANG
;
Kir Young KIM
Author Information
1. Department of Pediatrics, Yonsei University College of Medicine, Seoul, Korea. yangch22@yumc.yonsei.ac.kr
- Publication Type:Case Report
- Keywords:
Rhabdoid tumor;
Extrarenal
- MeSH:
Diagnosis;
Humans;
Infant;
Male;
Rhabdoid Tumor*
- From:Korean Journal of Pediatric Hematology-Oncology
2001;8(2):372-377
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Malignant rhabdoid tumor is a clinically aggressive neoplasm that was initially described as a distinctive renal tumor of childhood. But among the malignant rhabdoid tumors, extrarenal rhabdoid tumor is rare. We report an extrarenal neoplasm histologically and ultrastructurally identical to renal rhabdoid tumor that arose in the retroperitoneum of a 4-month-old boy and presented as a right lower abdominal mass. The tumor had an aggressive clinical course despite multimodal therapeutic regimens, and the patient died with disseminated disease 12 months after diagnosis.
