Case of Small Bowel Perforation due to Enteropathy-Type T-Cell Lymphoma.
10.3349/ymj.2009.50.6.859
- Author:
Yong Seok KIM
1
;
Yoo Shin CHOI
;
Jun Seok PARK
;
Beom Gyu KIM
;
Seong Jae CHA
;
Kyong Choun CHI
;
Sung Jun PARK
;
In Taik CHANG
;
Sung Il PARK
Author Information
1. Department of Surgery, College of Medicine, Chung-Ang University, Seoul, Korea. ushinchoi@hotmail.com
- Publication Type:Case Report
- Keywords:
Enteropathy-type T-cell lymphoma;
celiac disease;
intestinal perforation
- MeSH:
Aged;
Celiac Disease/*complications/pathology;
Female;
Gastrointestinal Neoplasms/*complications/pathology;
Humans;
Intestinal Perforation/*diagnosis/*etiology/pathology;
Lymphoma, T-Cell/*complications/pathology
- From:Yonsei Medical Journal
2009;50(6):859-861
- CountryRepublic of Korea
- Language:English
-
Abstract:
Enteropathy-type T-cell lymphoma (ETTL) is a rare disease with a poor prognosis. According to the World Health Organization (WHO) classification, it is a subtype of the peripheral T-cell lymphomas. This disease is associated with gluten-sensitive enteropathy, has a high risk of intestinal perforation and obstruction, and is refractory to chemotherapeutic treatment. We report the case of a 73-year-old woman who was diagnosed with enteropathy-type T-cell lymphoma of the small intestine, which was positive for the markers of cytotoxic T cells, CD3, CD8, and CD56, on immunohistochemical staining after resection of the perforated terminal ileum.