Mycosis Fungoides Palmaris et Plantaris in Children.
- Author:
Hwa Mi KIM
1
;
Jin Gu KIM
;
Chi Yeon KIM
Author Information
1. Department of Dermatology, School of Medicine, Gyeongsang National University and Gyeongsang Instiute of Health Science, Jinju, Korea. cykim@gnu.ac.kr
- Publication Type:Case Report
- Keywords:
Childhood;
Mycosis fungoides;
Palnaris et plantaris
- MeSH:
Child;
Dermatitis, Allergic Contact;
Dermatitis, Atopic;
Humans;
Middle Aged;
Mycosis Fungoides;
Organophosphorus Compounds;
PUVA Therapy;
Skin Diseases
- From:Korean Journal of Dermatology
2011;49(3):260-264
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Mycosis fungoides palmaris et plantaris (MFPP) is a rare form of mycosis fungoides that is confined to the palms and soles. The clinical manifestation of MFPP is often confused with inflammatory palmoplantar dermatoses. Mycosis fungoides is usually considered as a disease of middle age, but it is rarely developed at any age. A 10-year-old girl was referred to us with a 2-year history of recalcitrant palmoplantar dermatoses. Other clinics had treated her for more than 2 years, but all medical treatments turned out to have had no effect, despite her young age. She had not had any atopic dermatitis or allergic contact dermatitis. Histopathologic findings showed inflammatory cell infiltration and lymphocytic epidermotrophism. Monoclonal TCR-rearrangement was positive, so we diagnosed her as having MFPP. We tried to treat her with topical PUVA therapy and she improved within 3 months. Herein, we report on a case of mycosis fungoides Palmaris et plantaris in a 10-year-old girl that was treated successfully with topical PUVA.