A Case of Combined Double Chambered Right Ventricle and Discrete Subaortic Stenosis.
10.4070/kcj.1983.13.2.455
- Author:
Byung Woo YOON
;
Cheoul Ho KIM
;
Ki Ik KWON
;
Chong Hoon PARK
;
Myoung Mook LEE
;
Young Bae PARK
;
Yun Shik CHOI
;
Jung Don SEO
;
Young Woo LEE
;
Kyung Mo YOEN
- Publication Type:Case Report
- MeSH:
Adolescent;
Aorta;
Aortic Valve Insufficiency;
Discrete Subaortic Stenosis*;
Female;
Heart Ventricles*;
Humans;
Vena Cava, Superior
- From:Korean Circulation Journal
1983;13(2):455-462
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Combined double chambered right ventricle(DCRV) and discrete subaortic stenosis(DSAS) is a rare entity on which only 12 cases have been reported in the literature. We presented a case of combined DCRV and DSAS in an 18 year old girl. She had type II(thin membranous type) DSAS and the peak systolic prssure gradient between aorta and left ventricle was 38 mmHg. Aberrant muscle bundle was found on the right ventriculography and the pressure gradient in the right ventricle was 35 mmHg. She also had aortic regurgitation, persistent left sided superior vena cava and extracardiac malformations such as kyphoscoliosis and congenital cloacal anomaly.
