Bilateral Segmental Neurofibromatosis with Partial Unilateral Lentiginosis: Case Report with Review of the Literature.
10.5021/ad.2003.15.4.156
- Author:
You Jeong KIM
;
Mi Yeon KIM
;
Hyung Ok KIM
;
Young Min PARK
- Publication Type:Case Report
- Keywords:
Bilateral segmental neurofibromatosis;
Partial unilateral lentiginosis
- MeSH:
Female;
Humans;
Lentigo*;
Middle Aged;
Neurofibroma;
Neurofibromatoses*;
Neurofibromatosis 1;
Rare Diseases
- From:Annals of Dermatology
2003;15(4):156-159
- CountryRepublic of Korea
- Language:English
-
Abstract:
Bilateral segmental neurofibromatosis is a rare disease characterized by bilateral neurofibromas, with or without pigmented lesion, or unilateral neurofibromas with contralateral pigmented lesion, limited to a body segment. Partial unilateral lentiginosis is characterized by numerous lentigines localized to a body segment, often corresponding to one or more dermatome. Bilateral segmental neurofibromatosis combined with partial unilateral lentiginosis is very rare, and to our knowledge, only 2 cases have been reported in English literature. We herein report another case of bilateral segmental neurofibromatosis with partial unilateral lentiginosis in a 46-year-old woman.
