A Wedge-Shaped Anterior Hairline Extension Associated with a Tessier Number 10 Cleft.

Author: Hyung Min LEE ¹ ; Tae Kyung NOH ; Han Wook YOO ; Sung Bum KIM ; Chong Hyun WON ; Sung Eun CHANG ; Mi Woo LEE ; Jee Ho CHOI ; Kee Chan MOON
Author Information

1. Department of Dermatology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea. csesnumd@gmail.com
Publication Type:Case Report
Keywords: Anterior hairline extension; MOTA syndrome; Tessier number 10 cleft
MeSH: Abnormalities, Multiple; Anal Canal; Coloboma; Eyebrows; Eyelids; Fraser Syndrome; Hypertelorism; Manitoba; Scalp; Skin Manifestations
From:Annals of Dermatology 2012;24(4):464-467
CountryRepublic of Korea
Language:English
Abstract: A wedge-shaped anterior hairline extension is a very rare skin manifestation usually associated with congenital anomalies including a Tessier number 10 cleft. Other associated conditions are the Tessier number 9 cleft, the Fraser syndrome, and the Manitoba oculotrichoanal syndrome (MOTA syndrome). The Tessier number 10 cleft features include a coloboma of the middle third of the upper eyelid, and an eyebrow divided into two portions. The medial eyebrow portion may be absent and the lateral portion is angulated vertically, joining the hairline of the scalp. This creates a wedge-shaped anterior hairline extension. Herein we report on a case of a wedge-shaped anterior hairline extension associated with the Tessier number 10 cleft.