Pineal Anlage Tumor: A case report.
- Author:
Jong Sun CHOI
;
Hyung Jin SHIN
;
Yeon Lim SUH
- Publication Type:Case Report
- Keywords:
Pineal anlage tumor;
Pineoblastoma;
Melanotic neuroectodermal differentiation
- MeSH:
Brain;
Cartilage;
Child;
Female;
Ganglion Cysts;
Headache;
Humans;
Magnetic Resonance Imaging;
Muscle, Skeletal;
Neuroectodermal Tumor, Melanotic;
Pineal Gland;
Pinealoma;
Vomiting
- From:Korean Journal of Pathology
2000;34(12):1029-1033
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The term "pineal anlage tumor" has been recently proposed and few cases have been reported. We report the first Korean case of pineal anlage tumor in a 6-year-old girl who complained of headache and vomiting for 2 months. Brain MRI revealed a well defined, lobulated, calcifying mass in the pineal region. Tumor was totally removed. Pathological examination revealed a primitive pineal parenchymal tumor with melanotic epithelial component that was similar to histologic findings of melanotic neuroectodermal tumor of infancy, so-called retinal anlage tumor and of the developing pineal gland. The tumor was composed mostly of small, undifferentiated cells, Flexner-Wintersteiner rosettes, and ganglionic differentiation. The tumor also contained the cartilage and skeletal muscle cells.