A Case of Lipodystropha Centrifugalis Abdominalis Infantilis.
- Author:
Kang Woo LEE
;
Baik Kee CHO
;
Won HOUH
- Publication Type:Original Article
- MeSH:
Atrophy;
Biopsy;
Blood Cell Count;
Diagnosis;
Eccrine Glands;
Epidermis;
Erythema;
Histiocytes;
Humans;
Japan;
Lipodystrophy;
Liver Function Tests;
Lymphocytes;
Male;
Skin;
Thorax;
Urinalysis
- From:Korean Journal of Dermatology
1975;13(2):151-155
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Lipodystrophia centrifugalis ahdominalis infantilis(LCAI), an atypical form of progressive lipodystrophy, is a diseaee named by Imamura et al in 1971, and reported a few cases in japan. We report a case who has diagnosed as LCAI. The patient ia 5 and half year old boy. He had 2cm by 7cm sized, linear depressed leaion with surrounding erythema on the right inguinal region which was noticed 5 months prior to first diagnosis. There was no family history, no physical abnormality except skin lesion. Cornplete blood cell count, urinalysis, stool examination, liver function test and chest X-ray were within normal limit. Biopsy specimens from the depressed lesion and surrounding erythematous area revealed slight atrophy of the epidermis, a mild lymphocyte infiltration around the vesaels and eccrine glands in the upper part of derrnis, markedly decreased amount of subcutaneous adipoae tissue with mild lymph- ocyte infiltration in depressed area and marked lymphocyte infiltration, intermingled with histiocyte in surrounding erythematous area, but normal amount of adipase tissue.
