Anesthetic Experience of the Patient with Nemaline Myopathy: A case report.
10.4097/kjae.2000.38.5.940
- Author:
Jin Whan CHOI
1
;
Ji Young LEE
;
Hae Jin LEE
;
Jin Young CHON
;
Sung Jin HONG
;
Se Ho MOON
Author Information
1. Department of Anesthesiology, College of Medicine, The Catholic University of Korea, Seoul, Korea.
- Publication Type:Original Article
- Keywords:
Myopathy: nemaline myopathy
- MeSH:
Airway Obstruction;
Anesthesia;
Anesthesia, Epidural;
Congenital Abnormalities;
Humans;
Intubation;
Male;
Muscle, Skeletal;
Myopathies, Nemaline*;
Needles;
Respiratory Function Tests;
Vital Capacity;
Young Adult
- From:Korean Journal of Anesthesiology
2000;38(5):940-943
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Nemaline rod myopathy is an autosomal dominant disease characterized by nonprogressive symmetric skeletal muscle weakness affecting principally proximal skeletal muscles. Anesthesia of the patient with this disease is known to present some problems:difficult intubation due to facial dysmorphism, delayed onset of succinilcholine, reduced vital capacity on pulmonary function test and skeletal deformity. We anesthetized 19 year old male patient with nemaline myopathy for the operation of cryptochidism. Because of the possibility of difficult intubation, we produced epidural anesthesia with 20 G Tuohy needle at L5-S1 intervertebral space successfully. There were no problems in the course of operation and recovery except transient airway obstruction due to sedative.
