Atretic encephalocele/myelocele: case reports with emphasis on pathogenesis.
10.3346/jkms.1996.11.4.364
- Author:
Eun Kyung HONG
1
;
Nam Hoon KIM
;
Jung Dal LEE
Author Information
1. Department of Pathology, College of Medicine, Hanyang University, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Atretic encephalocele;
Atretic myelomeningocele;
cutaneous meningioma;
hamartoma;
pathogenesis
- MeSH:
Adult;
Case Report;
Child;
Encephalocele/*pathology;
Female;
Human;
Magnetic Resonance Imaging;
Mediastinal Neoplasms/*pathology;
Mediastinum/*pathology;
Meningomyelocele/*pathology;
Scalp/*pathology
- From:Journal of Korean Medical Science
1996;11(4):364-368
- CountryRepublic of Korea
- Language:English
-
Abstract:
Atretic encephaloceles or myelomeningoceles are frequently solid due to hamartomatous proliferation of fibrous tissue and blood vessels. Because of the fibrous nature of the tumor with no cystic cavity and unusual location with no connection to CNS, they are frequently regarded as insignificant hamartomas. Apart from this terminology, they are also described as cutaneous meningiomas or hamartomas with ectopic meningothelial elements by the presence of meningothelial cells. We report a case of atretic encephalocele in the parietal scalp of an 8 year-old boy and a case of myelomeningocele in the posterior mediastinum of a 31 year-old woman. The terms atretic encephalocele and myelomeningocele are more appropriate for these cases because they include their pathogenesis and the non-neoplastic nature of the lesion.
