Idiopathic Palmar Fasciitis with Polyarthritis Syndrome.
10.3346/jkms.2006.21.6.1128
- Author:
Yoon Kyoung SUNG
1
;
Moon Hyang PARK
;
Dae Hyun YOO
Author Information
1. Department of Internal Medicine, Division of Rheumatology and the Hospital for Rheumatic Diseases, Hanyang University Medical Center, 17 Haengdang-dong, Seongdong-gu, Seoul, Korea. dhyoo@hanyang.ac.kr
- Publication Type:Case Report ; Review
- Keywords:
Fasciitis;
Arthritis;
Malignancy
- MeSH:
Synovitis/*diagnosis;
Syndrome;
Humans;
Hand/*pathology;
Female;
Fasciitis/*diagnosis;
Arthritis/*diagnosis;
Adult
- From:Journal of Korean Medical Science
2006;21(6):1128-1132
- CountryRepublic of Korea
- Language:English
-
Abstract:
A 31-yr-old Korean woman was presented with 4-month history of bilateral hand swelling and stiffness. On clinical examination, she had a painful synovitis of both hands, wrists, knees and ankles. The radiologic and histological examinations confirmed it with palmar fasciitis and polyarthritis syndrome (PFPAS). PFPAS is an uncommon disorder characterized by progressive flexion contractures of both hands, inflammatory fasciitiis, fibrosis, and a generalized inflammatory arthritis. Although most reported cases of PFPAS have been associated with various malignancies, our patient have not been associated with malignancy during 24 months follow up period from her first symptom onset. Her symptoms were improved with moderate dose of corticosteroid and she is currently taking prednisone 5 mg daily without any evidence for internal malignancy. We present here in a young Korean patient with idiopathic PFPAS who was successfully treated with administration of corticosteroid.
