A Case of Mesenchymal Hamartoma Associated with Biliary Atresia.
- Author:
Kyung Dan CHOI
1
;
Jeong Kee SEO
;
Eon Woo SHIN
;
Jae Sung KO
;
Woo Sun KIM
;
Young Su PARK
;
Kyung Hoon KANG
;
Je Geun CHI
Author Information
1. Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Mesenchymal hamartoma;
Liver;
Biliary atresia;
Infant
- MeSH:
Biliary Atresia*;
Cholangitis;
Female;
Fibrosis;
Hamartoma*;
Humans;
Infant;
Liver;
Liver Transplantation;
Mesoderm;
Ultrasonography
- From:Korean Journal of Pediatric Gastroenterology and Nutrition
2001;4(1):113-119
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Mesenchymal hamartoma is an uncommon benign tumor usually found in childhood, especially during the first two years of life. The tumor consists of a solid component and multiple cyst. Without treatment, these lesions can grow to an enormous size. We experienced a case of mesenchymal hamartoma which was found incidentally, in a 8 month old girl who had ascending cholangitis after Kasai operation due to biliary atresia. On abdominal ultrasonography and CT, there was a well-defined homogeneous small echogenic mass in the right lobe of the liver with cirrhosis. Five months later, she underwent liver transplantation. Gross picture of the resected liver showed a dark greenish pigmented solid mass in the right lobe of the cirrhotic liver. Microscopic findings showed reactive mesenchyma and epithelial overgrowth.
