Anesthetic management of an adult patient with Rett syndrome and limited mouth opening: A case report.
10.4097/kjae.2011.61.5.428
- Author:
Ji Sung NHO
1
;
Dong Shik SHIN
;
Jee Youn MOON
;
Jae Woo YI
;
Jong Man KANG
;
Bong Jae LEE
;
Dong Ok KIM
;
Jun Young CHUNG
Author Information
1. Department of Anesthesiology and Pain Medicine, Kyung Hee University Hospital at Gangdong, College of Medicine, Kyung Hee University, Seoul, Korea. madsleep@naver.com
- Publication Type:Case Report
- Keywords:
Bronchoscopic intubation;
Limited mouth opening;
Rett syndrome
- MeSH:
Adult;
Airway Management;
Anesthesia, General;
Female;
Humans;
Intellectual Disability;
Mouth;
Movement Disorders;
Perioperative Period;
Respiration;
Rett Syndrome;
Seizures;
Young Adult
- From:Korean Journal of Anesthesiology
2011;61(5):428-430
- CountryRepublic of Korea
- Language:English
-
Abstract:
Rett syndrome is a neurological disease that occurs only in females and it manifests with mental retardation, seizures, movement disorders, autistic behavior and abnormal breathing. A 19-year-old female with Rett syndrome underwent ophthalmologic surgery under general anesthesia at our institution. Airway control was difficult due to her limited mouth opening. We recommend that anesthesiologists should have proper knowledge about this disease and the patients to avoid the complications and problems that can be encountered during the perioperative period.