Partial Anomalous Pulmonary Venous Return (PAPVR) in a Patient with Sjogren's Syndrome.
10.4078/jrd.2013.20.4.266
- Author:
Jennifer LEE
1
;
Honk Ki MIN
;
Keun Suk YANG
;
Hee Chul NAM
;
Hae Min LEE
;
Kyung Su PARK
;
Sung Hwan PARK
;
Ho Youn KIM
;
Seung Ki KWOK
Author Information
1. Division of Rheumatology, Department of Internal Medicine, School of Medicine, The Catholic University of Korea, Seoul, Korea. seungki73@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
PAPVR;
Pulmonary hypertension;
Sjogren's syndrome
- MeSH:
Dyspnea;
Heart;
Humans;
Hypertension, Pulmonary;
Lung Diseases, Interstitial;
Pulmonary Veins;
Sjogren's Syndrome
- From:Journal of Rheumatic Diseases
2013;20(4):266-269
- CountryRepublic of Korea
- Language:English
-
Abstract:
Pulmonary hypertension (PH) is a rare manifestation in patients with primary Sjogren's syndrome (pSS) and it can occur with or without interstitial lung disease (ILD). Patients with PH and ILD who show signs of exacerbation of dyspnea are commonly assessed for pure PH aggravation, ILD progression or pulmonary infection. However, the presence of congenital cardiac anomalies, such as partial anomalous pulmonary vein return (PAPVR), can also be a cause of dyspnea exacerbation. PAPVR is a rare congenital anomaly that involves drainage of 1 to 3 pulmonary veins into the right-sided heart circulation, resulting in a partial left-to-right shunt. Here we present a case of PAPVR as the cause of PH aggravation in a patient with pSS with accompanying PH.
