Abdominal Aortic Aneurysm in Marfan's Syndrome: Two Cases.
- Author:
Ji Hoon KIM
1
;
Tae Hyoung KIM
;
Sun Cheol PARK
;
Yong Sung WON
;
Sang Seob YUN
;
In Sung MOON
;
Jang Sang PARK
;
Seung Nam KIM
;
Yong Bok KOH
Author Information
1. Department of Surgery, Kangnam St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Seoul, Korea. sun60278@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
Marfan's syndrome;
Abdominal aortic aneurysm
- MeSH:
Adult;
Aorta;
Aortic Aneurysm;
Aortic Aneurysm, Abdominal*;
Cardiovascular System;
Connective Tissue;
Death, Sudden, Cardiac;
Dilatation;
Ethnic Groups;
Female;
Humans;
Incidence;
Marfan Syndrome*;
Mitral Valve;
Mitral Valve Insufficiency;
Rupture;
Thoracic Surgery
- From:Journal of the Korean Society for Vascular Surgery
2006;22(1):30-34
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Marfan syndrome is an inherited autosomal dominant disorder of the connective tissues, and the afflicted patients present with abnormalities of the skeletal, ocular, and cardiovascular system. The progressive dilatation of the proximal aorta leading to dissection and rupture is the typical feature and this can be a lethal complication of this disease. The incidence of Marfan syndrome is estimated to be 1 in 10,000 in most racial and ethnic groups. We experienced two cases of aortic aneurysm in Marfan syndrome. The first case was 32-year-old woman. She was admitted because of sudden onset of a painful abdominal mass for 2 days. Aortic aneurysm was diagnosed by CT and an echocardiogram showed severe mitral regurgitation (area ratio: 13/15). She underwent successful abdominal aortic aneurysm (AAA) repair and was discharged on postoperative 14th day; she was then prepared for open cardiac surgery for mitral valve replacement. The second case was 19- year-old woman. She was admitted with a known abdominal aortic aneurysm that she'd had for 1.5 years. She also underwent abdominal aortic aneurysm (AAA) repair that was technically successful, but she died on postoperative 10th day due to sudden cardiac arrest.
