- Author:
Ji Hoon CHOI
1
;
In Su AHN
;
Hee Bong LEE
;
Chun Wook PARK
;
Cheol Heon LEE
;
Hye Kunng AHN
Author Information
- Publication Type:Case Report
- Keywords: Churg-Strauss syndrome (CSS)
- MeSH: Antibodies, Antineutrophil Cytoplasmic; Asthma; Churg-Strauss Syndrome; Dermis; Eosinophilia; Eosinophils; Extremities; Humans; Leg; Male; Middle Aged; Neutrophils; Rhinitis; Rhinitis, Allergic, Perennial; Sensation; Sinusitis; Stress, Psychological; Vasculitis
- From:Annals of Dermatology 2009;21(2):213-216
- CountryRepublic of Korea
- Language:English
- Abstract: Churg-Strauss syndrome (CSS) or allergic granulomatosis angiitis is a rare primary vasculitic disease. CSS can be diagnosed by the presence of any four or more of the six criteria, which include asthma, eosinophilia greater than 10%, paranasal sinusitis, pulmonary infiltration, histological proof of vasculitis and mono- or poly-neuropathy. We report here on a 45-year-old male who developed erythematous macules, papules and hemorrhagic vesicles on both right extremities along with a tingling sensation and sacral pain. He has been suffering from recurrent allergic rhinitis and bronchial asthma for 6 months. The laboratory findings showed severe eosinophilia (22.3%), hyper-IgE and positivity for p-ANCA. On the histological examination of the hemorrhagic vesicle on the right lower leg, leukocytoclsatic vasulitis and many neutrophils and eosinophils around the cutaneous vessels were observed in the dermis.