Parry-Romberg Syndrome with Band-like Linear Alopecia.
- Author:
Seung Il CHOI
1
;
Jung Hoon YANG
;
Young Lip PARK
;
Jong Suk LEE
;
Kyu Uang WHANG
;
Sang Hoon LEE
Author Information
1. Department of Dermatology, Soonchunhyang University College of Medicine, Bucheon, Korea. shlee@schbc.ac.kr
- Publication Type:Case Report
- Keywords:
Facial hemiatrophy;
Linear scleroderma;
Parry-Romberg syndrome
- MeSH:
Alopecia;
Central Nervous System;
Collagen;
Facial Hemiatrophy;
Muscles;
Scalp;
Scleroderma, Localized;
Skin
- From:Korean Journal of Dermatology
2012;50(5):456-459
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Parry and Romberg described progressive facial hemiatrophy, characterized by progressive unilateral wasting of the skin, fat, muscle and bone in 1825 and 1846, respectively. Involvement of the central nervous system, with impairment of neurologic function, occurs infrequently. Linear scleroderma on frontal and parietal scalp, named 'en coup de sabre', is considered an overlapping condition. An 11 year-old girl was presented to our office with left facial hemiatrophy and transverse linear band-like alopecia on her posterior parietal scalp. Histopathologically, there was a sclerotic change of the collagen fibers and dermal lymphocytic infiltrations around the skin appendages. Her skin lesion has improved by intralesional corticosteroid injection. Linear scleroderma frequently coexists with Parry-Romberg syndrome. But in this case, she had a unique pattern of scleroderma, which is distinct from the previously reported cases.
