A Case of Childhood Dermatofibrosarcoma Protuberans.
- Author:
Young Min YOON
1
;
Sang Wook SON
;
Soo Hong SEO
;
Ae Ree KIM
;
Il Hwan KIM
Author Information
1. Department of Dermatology, Ansan Medical Center College of Medicine, Korea University Ansan, Korea. yymporsche@yahoo.co.kr
- Publication Type:Case Report
- Keywords:
Dermatofibrosarcoma protuberans;
CD34;
Childhood
- MeSH:
Child;
Continental Population Groups;
Dermatofibrosarcoma*;
Diagnosis, Differential;
Extremities;
Female;
Humans
- From:Korean Journal of Dermatology
2001;39(5):609-611
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Dermatofibrosarcoma protuberans(DFSP) is a rare cutaneous tumor, which occurs most commonly on the trunk or the proximal extremities, affects all races and often develops between the second and fifth decades of life. It is uncommon in childhood and is sometimes mistaken for a vascular lesion, as it often presents as a blue macule or small nodule. Histologically, it shows large uniformed spindle shaped cells arranged in a cartwheel or storiform pattern. Recently, the immunohistochemical staining with monoclonal antibody to CD34 is reported to give assistance in the differential diagnosis of DFSP from the fibrous or neural tumors. We report herein a case of childhood DFSP showing CD34 positivity in a 9-year-old girl
