A Case of Distal Renal Tubular Acidosis Associated with Medullary Sponge Kidney.
- Author:
Sung Jun JANG
1
;
Jo Yun JUNG
;
Jun Sik KIM
;
Heung Sik KIM
;
Hee Jung LEE
Author Information
1. Department of Pediatrics, School of Medicine, Keimyung University, Daegu, Korea.
- Publication Type:Case Report
- Keywords:
Medullary sponge kidney;
Distal renal tubular acidosis
- MeSH:
Acidosis;
Acidosis, Renal Tubular*;
Dilatation;
Humans;
Medullary Sponge Kidney*
- From:Journal of the Korean Pediatric Society
2001;44(1):89-93
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Renal tubular acidosis is a clinical state of systemic hyperchloremic acidosis resulting from impaired urine acidification. Medullary sponge kidney is a renal parenchymal malformation characterized by cystic dilatation of the collecting ducts. Although medullary sponge kidney is a congenital disease, it is rarely identified in childhood and is usually discovered in adulthood. Medullary sponge kidney patients may have defects in urinary acidification and concentration mechanism. We experienced a case of distal renal tubular acidosis associated with medullary sponge kidney. So, we report a case of distal renal tubular acidosis associated with medullary sponge kidney with a brief review of the related literature.
