A Case of diffuse dilatated coronary artery ectasia on Marfan's Syndrome.
- Author:
Dae Jung SHIM
1
;
Bum Soo KIM
;
Jin Ho KANG
;
Man Ho LEE
;
Jeong Ro PARK
;
Sang Jong LEE
;
Tae Un OH
;
Oun Ha JANG
;
Myung Sook KIM
Author Information
1. Department of Internal Medicine, Kangbuk Samsung Hospital, Collage of Medicine, Sungkyunkwan, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Marfan's syndrome;
Coronary artery ectasia
- MeSH:
Adult;
Aneurysm;
Connective Tissue;
Coronary Artery Disease;
Coronary Vessels*;
Dilatation, Pathologic*;
Ehlers-Danlos Syndrome;
Heart;
Humans;
Male;
Marfan Syndrome*;
Prevalence;
Syphilis
- From:Korean Journal of Medicine
1998;54(6):867-872
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Marfan's syndrome is a an autosomal dominant disorder of connective tissue that is characterized by ocular, skeletal, and cardiovascular manifestation. It is estimated to have a prevalence of 4-6 per 10,000 people, and at least 25 percent of the cases occur in the absence of a family history. Coronary artery ectasia is a diffuse abnormality of the vessel wall, which has been reported in associated with coronary atherosclerosis, infectious process, congenital heart lesion, syphilis, Ehlers-Danlos syndrome. We reported a case of 25-year-old male who presented with Marfan's syndrome associated with dissecting ascending arotic aneurysm and diffuse dilatated coronary artery ectasia. Coronary angiographic study demonstrated the diffusely dilatated coronary artery ectasia.
